ICD-10-CM Book 2025 Edition
Chapters ICD-10-CM Book Table of Content /
Q80-Q89 Other congenital malformations /
Q82 Other congenital malformations of skin
Billable ICD-10-CM Code Q82.2
Q82.2
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Congenital cutaneous mastocytosis 
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Congenital diffuse cutaneous mastocytosis
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Congenital maculopapular cutaneous mastocytosis
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Congenital urticaria pigmentosa
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excludes1
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cutaneous mastocytosis NOS (D47.01) |
diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01) |
malignant mastocytosis (C96.2-) |
systemic mastocytosis (D47.02) |
urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01) |
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