ICD-10-CM Book 2025 Edition
Chapters ICD-10-CM Book Table of Content /
E76 Disorders of glycosaminoglycan metabolism
Billable ICD-10-CM Code E76.22
E76.22
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Sanfilippo mucopolysaccharidoses 
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Mucopolysaccharidosis, type III (A) (B) (C) (D)
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Sanfilippo A syndrome
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Sanfilippo B syndrome
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Sanfilippo C syndrome
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Sanfilippo D syndrome
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