D56 |
 |
Thalassemia |
| |
Excludes1 |
sickle-cell thalassemia (D57.4-)
|
|
| |
D56.0 |
 |
Alpha thalassemia |
| |
Alpha thalassemia major | Hemoglobin H Constant Spring | Hemoglobin H disease | Hydrops fetalis due to alpha thalassemia | Severe alpha thalassemia | Triple gene defect alpha thalassemia |
UseAdditionalCode |
code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)
|
Excludes1 |
alpha thalassemia trait or minor (D56.3) asymptomatic alpha thalassemia (D56.3) hydrops fetalis due to isoimmunization (P56.0) hydrops fetalis not due to immune hemolysis (P83.2)
|
|
|
| |
D56.1 |
 |
Beta thalassemia |
| |
Beta thalassemia major | Cooley's anemia | Homozygous beta thalassemia | Severe beta thalassemia | Thalassemia intermedia | Thalassemia major |
Excludes1 |
beta thalassemia minor (D56.3) beta thalassemia trait (D56.3) delta-beta thalassemia (D56.2) hemoglobin E-beta thalassemia (D56.5) sickle-cell beta thalassemia (D57.4-)
|
|
|
| |
D56.2 |
 |
Delta-beta thalassemia |
| |
Homozygous delta-beta thalassemia |
Excludes1 |
delta-beta thalassemia minor (D56.3) delta-beta thalassemia trait (D56.3)
|
|
|
| |
D56.3 |
 |
Thalassemia minor |
| |
Alpha thalassemia minor | Alpha thalassemia silent carrier | Alpha thalassemia trait | Beta thalassemia minor | Beta thalassemia trait | Delta-beta thalassemia minor | Delta-beta thalassemia trait | Thalassemia trait NOS |
Excludes1 |
alpha thalassemia (D56.0) beta thalassemia (D56.1) delta-beta thalassemia (D56.2) hemoglobin E-beta thalassemia (D56.5) sickle-cell trait (D57.3)
|
|
|
| |
D56.4 |
|
Hereditary persistence of fetal hemoglobin [HPFH] |
|
| |
D56.5 |
 |
Hemoglobin E-beta thalassemia |
| |
Excludes1 |
beta thalassemia (D56.1) beta thalassemia minor (D56.3) beta thalassemia trait (D56.3) delta-beta thalassemia (D56.2) delta-beta thalassemia trait (D56.3) hemoglobin E disease (D58.2) other hemoglobinopathies (D58.2) sickle-cell beta thalassemia (D57.4-)
|
|
|
| |
D56.8 |
 |
Other thalassemias |
| |
Dominant thalassemia | Hemoglobin C thalassemia | Mixed thalassemia | Thalassemia with other hemoglobinopathy |
Excludes1 |
hemoglobin C disease (D58.2) hemoglobin E disease (D58.2) other hemoglobinopathies (D58.2) sickle-cell anemia (D57.-) sickle-cell thalassemia (D57.4-)
|
|
|
| |
D56.9 |
 |
Thalassemia, unspecified |
| |
Mediterranean anemia (with other hemoglobinopathy) |
|
|