D55 |
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Anemia due to enzyme disorders  |
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Excludes1 |
drug-induced enzyme deficiency anemia (D59.2)
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D55.0 |
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Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency |
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Favism | G6PD deficiency anemia |
Excludes1 |
glucose-6-phosphate dehydrogenase (G6PD) deficiency without anemia (D75.A)
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D55.1 |
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Anemia due to other disorders of glutathione metabolism |
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Anemia (due to) enzyme deficiencies, except G6PD, related to the hexose monophosphate [HMP] shunt pathway | Anemia (due to) hemolytic nonspherocytic (hereditary), type I |
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D55.2 |
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Anemia due to disorders of glycolytic enzymes |
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Excludes1 |
disorders of glycolysis not associated with anemia (E74.81-)
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D55.21 |
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Anemia due to pyruvate kinase deficiency |
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PK deficiency anemia | Pyruvate kinase deficiency anemia |
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D55.29 |
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Anemia due to other disorders of glycolytic enzymes |
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Hexokinase deficiency anemia | Triose-phosphate isomerase deficiency anemia |
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D55.3 |
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Anemia due to disorders of nucleotide metabolism |
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D55.8 |
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Other anemias due to enzyme disorders |
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D55.9 |
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Anemia due to enzyme disorder, unspecified |
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